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Vagus nerve stimulator used for epilepsy also improves symptoms of rheumatoid arthritis

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Adverse events require further study

The many different functions and brain regions associated with the vagus nerve have led researchers to test its usefulness in treating several illnesses, including epilepsy, treatment-resistant depression, anxiety disorders, Alzheimer’s disease, migraines, fibromyalgia, obesity, and tinnitus.

The Food and Drug Administration’s approval of a vagus nerve stimulator (VNS) subsequent to a 1997 neurological devices panel meeting has remained controversial. In the only randomized, controlled trial of severe depression, VNS failed to perform any better when turned on than in otherwise similarly implanted patients whose device was not turned on, according to the agency’s summary of the data.

Dr. Maurizio Cutolo

However, the discovery in 2007 by Kevin J. Tracey that vagus nerve stimulation inhibits inflammation by suppressing pro-inflammatory cytokine production (inflammatory reflex) has led to significant interest in the potential to use this approach for treating inflammatory diseases ranging from arthritis to colitis, ischemia, myocardial infarction, and heart failure (J Clin Invest. 2007;117[2]:289-96).

At present, the study by Dr. Koopman and her colleagues showed that vagus nerve stimulation (up to four times daily) by the implantable VNS in rheumatoid arthritis (RA) patients significantly inhibited tumor necrosis factor (TNF) production for up to 84 days. RA disease severity apparently improved significantly. The results of this investigation seem to confirm the crucial role played by the neuroendocrine immune system network in RA (Nat Rev Rheumatol. 2011;7[9]:500-2).

However, the question now is: Are there issues and limitations about this possible new approach to RA treatment based on previous experiences? An obvious issue is the limited number of adverse events reported by the authors.

In contrast, adverse events have been signaled in all previous studies for VNS use as expected: cardiac arrhythmia during implantation, intermittent decrease in respiratory flow during sleep, posttreatment increase of apnea hypopnea index, and the development of posttreatment mild obstructive sleep apnea in up to one-third of patients, a minority of whom develop severe obstructive sleep apnea clearly related to VNS therapy. Another study has shown alteration of voice in 66%, coughing in 45%, pharyngitis in 35%, and throat pain in 28% (Pediatr Neurol. 2008;38[2]:99-103). Other reports of VNS device adverse events range from hoarseness (very common) to frank laryngeal muscle spasm and upper airway obstruction (rare). Other nonspecific symptoms include headache, nausea, vomiting, dyspepsia, dyspnea, and paresthesia.

At present, the approach of VNS therapy in RA needs further strict investigations, especially regarding the large number of potential adverse events expected. In addition, the target of reducing TNF levels in RA patients is already obtainable with several other noninvasive and established treatments.

Maurizio Cutolo, MD, is professor of rheumatology and internal medicine and director of the research laboratories and academic division of clinical rheumatology in the department of internal medicine at the University of Genova (Italy). He has no relevant disclosures.


 

FROM PNAS

References

An implanted vagus nerve stimulator like that used for epilepsy treatment reduced inflammatory markers and significantly improved symptoms and function in a small cohort of patients with rheumatoid arthritis.

After 42 days, almost 30% of patients had achieved disease remission, Frieda A. Koopman, MD, and her colleagues reported in the July issue of the Proceedings of the National Academy of Science (doi: 10.1073/pnas.1605635113). The improvements disappeared rapidly when the devices were turned off, but were quickly reestablished after stimulation resumed.

“This first-in-class study supports a conceptual framework for further studies of electronic medical devices in diseases currently treated with drugs, an approach termed ‘bioelectronic medicine,’” wrote Dr. Koopman of the University of Amsterdam, and her coauthors.

The team built on evidence of what they termed a “reflex neural circuit” in the vagus that strongly influences the production of inflammatory cytokines. Animal studies showed that electrical stimulation of the vagus nerve encouraged choline acetyltransferase–positive T cells to secrete acetylcholine in the spleen and other tissues. Acetylcholine binds to a class of nicotinic receptors on monocytes, macrophages, and stromal cells, and inhibits their inflammatory response.

“Inflammatory reflex signaling, which is enhanced by electrically stimulating the vagus nerve, significantly reduces cytokine production and attenuates disease severity in experimental models of endotoxemia, sepsis, colitis, and other preclinical animal models of inflammatory syndromes,” the team noted.

The group reported on two human studies, totaling 25 patients. The first comprised seven patients with epilepsy who received the implanted vagus nerve stimulator for medically refractory seizures. None of these patients had a history of RA or any other inflammatory disease. The second group was all patients with active RA.

Each epilepsy patient contributed peripheral blood for study, which was collected before, during and after the implantation surgery. The team studied inflammatory markers by adding endotoxin to the samples. Those collected after the patient had been exposed to a single 30-second stimulation at 20 Hertz showed significantly inhibited production of TNF-alpha, compared with that seen in unexposed blood. Interleukin (IL)-6 and IL-1beta was also inhibited significantly by vagus nerve stimulation.

The next study involved 17 patients who had active RA, but not epilepsy. Of these, seven had failed methotrexate but were naïve to biologics; the rest had failed methotrexate and at least two biologics from different classes. Their average disease duration was 11 years.

The 86-day study gradually titrated the stimulation dose, but even at its highest, stimulation was far less than what is typically employed in epilepsy, “in which current is delivered at 60-second intervals, followed by an off interval of 5-180 minutes, repeated continuously,” the investigators wrote. “Thus, epilepsy patients may receive electrical current delivery for up to 240 minutes daily. Preclinical studies have established that stimulation of the inflammatory reflex for as little as 60 seconds confers significant inhibition of cytokine production for up to 24 hours.”

There was a 14-day post-implantation washout period with no stimulation, followed by 28 days of treatment titration. During that time, stimulation was ramped up from single 60-second stimulation with electric pulses of 250-microseconds duration at 10 Hertz and an output current between 0.25-2.0 milliamps, to the highest amperage tolerated (up to 2.0 milliamps).

That dose was the treatment target, and delivered once daily for 60 seconds in 250-microsecond pulse widths at 10 Hertz. At day 28, patients who had not had good clinical response according to EULAR response criteria, had their stimulation increased to four times daily.

In the group of seven methotrexate-resistant patients, two received electric current pulses four times daily. In the group of 10 methotrexate- and biologic-resistant patients, 6 received the four-dose stimulation.

On day 42, TNF-alpha levels in cultured peripheral blood were significantly reduced from baseline.

At that time, the vagus nerve stimulator was turned off for 14 days. By the end of the silent period, TNF-alpha levels had risen significantly from the day 42 levels. The stimulator was restarted on day 56. By day 84, after 28 more days of stimulation, TNF-alpha levels had again decreased significantly.

Symptoms and function as measured by the Disease Activity Score 28 followed a similar trajectory, improving during the initial treatment, worsening during the period of no stimulation, and improving again when stimulation was restarted. Symptom and function scores correlated positively with change in TNF levels.

The investigators also assessed the response rates according to American College of Rheumatology criteria. At day 42, 71% of those in the methotrexate-resistant group had achieved a 20% response; 57% a 50% response; and 28.6% a 70% response. Response was not as dramatic in the group resistant to both drug classes: rates were 70%, 30%, and 0%.

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