Immunoglobulin A Pemphigus Involving the Perianal Skin and Oral Mucosa: An Unusual Presentation

Immunoglobulin A (IgA) pemphigus is a rare autoimmune blistering disease characterized by epidermal acantholysis and neutrophilic infiltrates, as well as intraepidermal IgA deposits. We report an unusual case of IgA pemphigus involving anal/perianal skin and oral mucosa that demonstrated a successful response to dapsone treatment.