Pediatric Dermatology
A "Hyperextensive" Review of Ehlers-Danlos Syndrome
Cutis. 2008 October;82(4):242-248
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Fernandes NF, Schwartz RA
Ehlers-Danlos syndrome (EDS) is a heterogeneous group of connective tissure disorders characterized by hyperextensibility, delayed wound healing, joint hypermobility, thin skin, easy bruising, tissue fragility, "cigarette-paper" scarring over bony prominences, mitral valve prolapse, and other findings. There are 6 main types of EDS. Regardless of presentation as a chief concern or an incidental finding, physicians should be aware that the prominent skin findings of EDS are cutaneous signs of an important systemic disorder.