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AHA/ACC: Consensus recommendations for young athletes with congenital heart disease

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Avoiding ‘one size fits all’

For many busy clinicians, societal guidelines, task force recommendations, expert consensus statements, and similar authoritative tomes are resources that are scarcely ever read carefully. This is likely not a reflection of the inherent value of such documents, but rather related to the observation that updated guidelines generally reflect, at most, a small change from predecessor versions. (It also should be mentioned that many such contributions are fairly heavy going for even the most determined reader.)

Occasionally, however, a new guideline may signal a dramatic shift in practice, and the recently published AHA/ACC Scientific Statement on Eligibility and Disqualification Recommendations for Competitive Athletes with Cardiovascular Abnormalities (Congenital Heart Disease) contains such a change.

Dr. Robert Jaquiss

In particular, the new recommendation suggests that athletes with anomalous aortic origin of the right coronary from the left coronary sinus, who have neither symptoms nor a positive stress test, may be allowed to participate in competitive athletics without undergoing surgical repair. As before, those with anomalous left coronary should not be allowed to participate until after surgical treatment.

Prior guidelines suggested that all patients, both anomalous left from right sinus and right from left sinus, be restricted prior to surgery. Because anomalous right coronary is five to six times more common than anomalous left coronary and because it is certainly much less ominous, the previous “one size fits all” approach almost certainly resulted in overtreatment, unnecessary restriction of participation, or both. Furthermore, because anomalous aortic of a coronary artery is so common, occurring in 0.1%-0.2% of the population (300,000 to 600,000 people in the United States), many thousands of competitive athletes will be impacted by the changed guidelines.

Most cardiologists, surgeons, and, most especially, patients will welcome the updated recommendations. Nonetheless, it must be emphasized that anomalous coronary arteries, even anomalous right coronary arteries, may indicate an increased risk of sudden death and that a complete assessment, including stress testing when feasible, and thorough discussion with expert clinicians is still absolutely necessary for such patients and their families.

Dr. Robert Jaquiss of Duke University, Durham, N.C., is the congenital heart section associate medical editor for Thoracic Surgery News.


 

FROM THE JOURNAL OF THE AMERICAN COLLEGE OF CARDIOLOGY

References

Coarctation of the aorta: Treated and untreated

Before a decision is made regarding exercise participation, a detailed evaluation should be conducted, including a physical examination, ECG, chest radiograph, exercise testing, transthoracic echocardiographic evaluation of the aortic valve and aorta, and either magnetic resonance imaging or computed tomography angiography, according to the committee. The determination as to the level of sports participation permitted requires a complex assessment of these various test results and can range from full participation in the case of the least affected to restrictions to low-intensity sports in those more severely affected.

Cyanotic CHD, including tetralogy of Fallot

Full clinical assessment, including laboratory and exercise testing, should be considered before any physical activity because this population is at very high risk of sudden death, according to the committee. Recommendations are complex and depend on the level of repair and its success, but, in general, significant restrictions are recommended for all but the most effectively treated patients.

Transposition of the great arteries after atrial switch (Mustard or Senning operation)

This is a population highly at risk, according to the committee. They appear to have a unique response to exercise with reports that a high proportion of sudden death events occur during exertion. In addition, evidence of exercise-induced arrhythmias on routine clinical testing has not been shown to reliably predict exercise-induced SCD events. Although recommendations vary, including strong restrictions for many, at best the most successful of these patients should only be considered for low- to moderate-intensity competitive sports, according to the committee.

Other conditions assessed and evaluated by the committee included congenitally corrected TGA, TGA after the arterial switch, Fontan procedure, elevated pulmonary vascular resistence in CHD, ventricular dysfunction after CHD surgery, and Ebstein anomaly of the tricuspid valve.

In all cases, complete physical assessment of these patients is recommended, especially due to the often highly individualized nature of the patient’s presentation of these conditions and the variety and variability of interventions that may have been performed. Such differentials make recommendations regarding sports participation a complex calculus, which the committee attempts to provide, listing whatever evidence is available.

The majority of these patients, however, will not be considered for the highest levels of competitive sports participation. Although, in almost all cases, the need for physical activity as a contributor to patient health and well-being is stressed at whatever level of performance is possible.

The report ”Eligibility and disqualification recommendations for competitive athletes with cardiovascular abnormalities: Task Force 4: congenital heart disease: a scientific statement from the American Heart Association and American College of Cardiology,” was prepared by Dr. Van Hare and his colleagues on behalf of the American Heart Association Electrocardiography and Arrhythmias Committee of the Council on Clinical Cardiology, Council on Cardiovascular Disease in the Young, Council on Cardiovascular and Stroke Nursing, Council on Functional Genomics and Translational Biology, and the American College of Cardiology (doi: 10.1016/j.jacc.2015.09.032).

This report is one of the assessments and recommendations of 15 task forces on eligibility and disqualification recommendations for young athletes, nine of which are disease or multidisease related. The other six task forces focus on a variety of relevant topics and issues regarding the risks of young athletes on the field, including screening, the use of automated external defibrillators on the field, the use of dietary supplements and performance-enhancing drugs, sudden death, and the medical-legal perspectives involved.

All 15 task force reports were simultaneously published online in the Journal of the American College of Cardiology and the journal Circulation.

Dr. Van Hare and all but one member of the writing group had no disclosures. One member disclosed consultant/advisory committee associations with a variety of medical device companies.

mlesney@frontlinemedcom.com

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