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Gene Therapy for Certain Types of ALL Approved

Novartis news release; 2017 Aug 30

The FDA has approved the first gene therapy for certain pediatric and young adult patients with a form of acute lymphoblastic leukemia (ALL).

Indications: Kymriah is a CD19-directed genetically modified autologous T cell immunotherapy indicated for the treatment of patients up to 25 years of age with B-cell precursor ALL that is refractory or in second or later relapse.

Dosage and administration:

  • For patients 50 kg or less, 0.2 to 5.0 x 106 chimeric antigen receptor (CAR)-positive viable T cells per kg body weight intravenously.
  • For patients above 50 kg, 0.1 to 2.5 x 108 total CAR-positive viable T cells (non-weight based) intravenously.

Efficacy and safety: Approval is based on trial results showing that the overall remission rate within 3 months of treatment was 83%.

Side effects/risks: The most common adverse reactions are cytokine release syndrome, hypogammaglobulinemia, infections-pathogen unspecified, pyrexia, decreased appetite, headache, encephalopathy, hypotension, bleeding episodes, tachycardia, nausea, diarrhea, vomiting, viral infectious disorders, hypoxia, fatigue, acute kidney injury, and delirium.

Citation:

FDA approval brings first gene therapy to the United States [news release]. Silver Spring, MD: FDA. August 30, 2017. https://www.fda.gov/NewsEvents/Newsroom/PressAnnouncements/ucm574058.htm. Accessed September 4, 2017.

Kymriah [package insert]. East Hanover, NJ: Novartis Pharmaceuticals Corporation. 2017. https://www.pharma.us.novartis.com/sites/www.pharma.us.novartis.com/files/kymriah.pdf. Accessed September 4, 2017.